Ionis Pharmaceuticals

Ionis Pharmaceuticals works on 19 rare diseases tracked on Trial Friend, including Acromegaly, Alexander Disease, Amyotrophic Lateral Sclerosis and 16 more, with 15 recruiting clinical trials and 2 FDA-approved rare disease drugs.

Ionis Pharmaceuticals is a leader in antisense oligonucleotide (ASO) therapies targeting RNA for rare genetic, neurological, and cardiovascular diseases. Approved products include Tryngolza (olezarsen) for familial chylomicronemia syndrome (2024), Dawnzera (donidalorsen) for hereditary angioedema (2025), and Zanvastro (zilganersen), approved in September 2026 as the first and only treatment for Alexander disease. Through its partnership with Biogen, Ionis developed tofersen (Qalsody) for SOD1-ALS and Spinraza for spinal muscular atrophy. The pipeline includes ION582 for Angelman syndrome (Phase 3) and sefaxersen, partnered with Roche, for IgA nephropathy, which met its primary proteinuria endpoint at a prespecified interim analysis of the Phase 3 IMAgINATION study in September 2026.

Type
Diversified Pharma
Ticker
IONS
Headquarters
Carlsbad, United States
Founded
1989
Website
ionis.com
15
Active Rare Disease Trials
2
Approved Rare Disease Drugs
19
Rare Diseases in Portfolio
37
Years Active

Ionis Pharmaceuticals Drug Pipeline

Ionis Pharmaceuticals has 15 active clinical trials across 4 development stages, with 15 currently recruiting participants. Clinical trials advance through phases: Phase 1 tests safety in a small group, Phase 2 evaluates effectiveness and side effects, Phase 3 confirms benefit in a larger population, and Phase 4 monitors long-term safety after FDA approval.

Note: This pipeline includes all of Ionis Pharmaceuticals's active interventional trials, not only those targeting rare diseases. We show the full pipeline because a company's broader research activity, therapeutic expertise, and development infrastructure directly shape its ability to advance rare disease programs. A strong overall pipeline often signals deeper clinical operations, faster enrollment capabilities, and greater commitment to bringing new treatments to patients.

Understand Ionis Pharmaceuticals's pipeline
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1
Early Phase / Phase 11 trial
3
Phase 23 trials
Recruiting
Methyl CpG Binding Protein 2 (MECP2) Duplication Syndrome
Recruiting
10
Phase 310 trials
1
Other1 trial

Ionis Pharmaceuticals Clinical Trials (15)

Active and recruiting clinical trials sponsored by Ionis Pharmaceuticals, sourced live from ClinicalTrials.gov. Each trial card shows the study phase, current recruitment status, conditions under investigation, study locations, eligibility criteria, and a direct link to the full ClinicalTrials.gov record. You can also download a one-page PDF summary to share with your doctor.

Note: Recruitment statuses on ClinicalTrials.gov may not immediately reflect recent FDA decisions, sponsor announcements, or enrollment changes. Always confirm a trial's current status directly with the study coordinator.

Ask about Ionis Pharmaceuticals's trials
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ACTIVE NOT RECRUITINGPHASE3Recently updatedNCT06914609

REVEAL: A Phase 3 Study of Obudanersen (ION582) in Angelman Syndrome

Intervention: obudanersen, Placebo

The purpose of this study is to evaluate the efficacy and safety of obudanersen in children and adults with Angelman syndrome caused by a deletion or mutation of the UBE3A gene.

Ages 2 Years - 50 Years41 locations
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RECRUITINGPHASE3Recently updatedNCT07782827

CHAMPION: A Study to Evaluate the Efficacy and Safety of Obudanersen (ION582) in Children and Adults With Angelman Syndrome (AS)

Intervention: obudanersen

The primary purpose of the study is to evaluate efficacy of obudanersen in participants with AS due to uniparental disomy or imprinting defects (UPD/ID) as measured through expressive communication.

Ages 2 Years - 50 Years1 location
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RECRUITINGPHASE1, PHASE2Recently updatedNCT07531745

ASCEND: Safety and Tolerability of ION337 for the Treatment of Dravet Syndrome

Intervention: ION337

The primary purpose of this study is to evaluate the safety and tolerability of ION337 in participants with Dravet syndrome (DS).

Ages 2 Years - 12 Years6 locations
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RECRUITINGPHASE3Recently updatedNCT07298447

Donidalorsen Treatment in Children With Hereditary Angioedema

Intervention: Donidalorsen

The purpose of this study is to evaluate the safety, tolerability and pharmacokinetics of donidalorsen in pediatric participants with hereditary angioedema (HAE) Type I (HAE-1) or Type II (HAE-2).

Ages 2 Years - 11 Years16 locations
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RECRUITINGPHASE3Recently updatedNCT07727538

A Study of Olezarsen for the Treatment of Familial Chylomicronemia Syndrome (FCS) in Pediatric Participants

Intervention: Olezarsen

The primary purpose of the study is to evaluate the efficacy of olezarsen administered by subcutaneous injection to pediatric participants with FCS.

Ages 2 Years - 17 Years4 locations
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ACTIVE NOT RECRUITINGPHASE3Recently updatedNCT04849741

A Study to Evaluate the Safety and Efficacy of Zilganersen (ION373) in Patients With Alexander Disease (AxD)

Intervention: zilganersen, Placebo

The purpose of this study is to evaluate the safety and efficacy of zilganersen (ION373) in improving or stabilizing gross motor function across the full range of affected domains in patients with AxD.

Ages 2 Years - 65 Years13 locations
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ACTIVE NOT RECRUITINGPHASE1, PHASE2Recently updatedNCT05127226

HALOS: A Safety, Tolerability, Pharmacokinetics and Pharmacodynamics Study of Multiple Ascending Doses of ION582 in Participants With Angelman Syndrome

Intervention: ION582

The purpose of this study is to evaluate the safety and tolerability of ascending doses of ION582 administered intrathecally in participants with Angelman syndrome.

Ages 0 Years - 50 Years11 locations
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Ionis Pharmaceuticals FDA-Approved Drugs (2)

Medications developed or marketed by Ionis Pharmaceuticals that have received U.S. Food and Drug Administration approval. Drug data is sourced from the openFDA database and includes brand names, generic names, approval dates, and matched rare disease indications. Where a drug treats a condition covered by Trial Friend, the disease name links directly to that disease page.

Drug NameBrand NameRare DiseasesApproval Date
DONIDALORSENDAWNZERA
subcutaneous
Aug 21, 2025
OLEZARSEN SODIUMTRYNGOLZA
subcutaneous
Dec 19, 2024

Ionis Pharmaceuticals Trial Locations

Ionis Pharmaceuticals clinical trials are running at 265 sites in 29 countries. Click any country to drill down by state, city, and individual research facility. Proximity to a trial site is one of the most important factors in deciding whether to participate.

United States
98▼
Canada
21▼
Italy
21▼
Spain
15▼
United Kingdom
14▼
France
13▼
Germany
12▼
Australia
9▼
Israel
6▼
Netherlands
5▼
Brazil
5▼
Taiwan
5▼

Rare Disease Focus Areas (19)

Diseases targeted by Ionis Pharmaceuticals's clinical trial and drug development programs

AcromegalyEndocrine & Hormonal

Acromegaly is a rare hormonal disorder caused by excessive growth hormone production, typically from a pituitary adenoma, resulting in abnormal growth of hands, feet, and facial features. It also caus...

Prevalence: Approximately 50-130 cases per million people; estimated 25,000-30,000 people in the United States with about 3,000 new cases diagnosed per year
Alexander DiseaseNeurological & Neuromuscular

Alexander disease is a rare inherited leukodystrophy caused by mutations in the GFAP gene affecting astrocyte function. The condition leads to progressive neurological deterioration with abnormal prot...

Prevalence: Approximately 1 in 100,000 to 200,000 people
Amyotrophic Lateral SclerosisNeurological & Neuromuscular

Amyotrophic lateral sclerosis is a progressive neurodegenerative disease destroying motor neurons in the brain and spinal cord. This causes progressive weakness and paralysis of voluntary muscles whil...

Prevalence: About 5,000 new cases per year in the U.S.; approximately 16,000 Americans living with ALS at any given time
Angelman SyndromeNeurological & Neuromuscular

Angelman Syndrome is a rare neurological disorder caused by loss of function of the UBE3A gene on the maternal chromosome 15. People with this condition typically develop normal until 6-12 months of a...

Prevalence: Approximately 1 in 12,000 to 20,000 people
ATTR Amyloidosis (Transthyretin Amyloidosis)Metabolic & Lysosomal

ATTR amyloidosis is a rare progressive disease where abnormal transthyretin protein accumulates as amyloid deposits in the heart, nerves, and other organs. It can be inherited (hereditary ATTR) or dev...

Prevalence: Approximately 5,000 to 7,000 new cases diagnosed annually in the U.S.
Cystic FibrosisPulmonary & Respiratory

Cystic fibrosis is an autosomal recessive genetic disorder affecting the CFTR protein, which normally regulates chloride transport. Defective CFTR causes thick, sticky secretions in the lungs and dige...

Prevalence: About 30,000 people in the U.S.; 1 in 2,500 to 3,500 births among Caucasians

Patient Resources

Organizations and resources related to Ionis Pharmaceuticals's rare disease focus areas

Frequently Asked Questions About Ionis Pharmaceuticals

Common questions about Ionis Pharmaceuticals's rare disease programs, clinical trials, and treatments.