NF1 Gene and Neurofibromatosis Type 1: Mutations and Clinical Trials

The NF1 gene sits on chromosome 17q11.2, and its full name is neurofibromin 1. Orphanet links NF1 to 11 rare conditions and lists variants in the gene as a cause of 8 of them. Trial Friend's Neurofibromatosis Type 1 and Pheochromocytoma pages list NF1 among the genes behind each condition. As of September 29, 2026, 16 recruiting or soon-opening trials on ClinicalTrials.gov name NF1 as a gene.

See the trialsSearch another gene

What the NF1 gene does

NF1 makes neurofibromin, a tumor suppressor protein. It helps keep cells from growing and dividing too fast by turning off a growth-signaling protein called Ras.

Summarized from the NF1 page on MedlinePlus Genetics, U.S. National Library of Medicine, checked September 29, 2026.

Conditions linked to NF1 on Trial Friend

These condition pages list NF1 among the genes behind the condition, checked against genetics references when each page was written.

Neurofibromatosis Type 1

One disease-causing variant can be enough to cause the condition.

About half of cases are de novo NF1 variants; the diagnosis can be made clinically, with NF1 testing used to confirm.

Pheochromocytoma

One disease-causing variant can be enough to cause the condition.

About 35% of cases are hereditary, so germline panel testing is recommended for essentially all patients.

NF1 mutation clinical trials

These recruiting or soon-opening trials mention NF1 as a gene in their title, summary, eligibility rules or keywords. Some want people with a variant in it, and others study it more broadly, which is why each trial's own words are shown. In cancer trials the gene change is usually one found in the tumor rather than one a person inherited.

16 trials, checked September 29, 2026. The list refreshes from ClinicalTrials.gov every few hours.

RecruitingPhase 2NCT07237100
Mirdametinib in Patients With Advanced NF1-mutant Melanoma
Advanced Unresectable Melanoma · Metastatic Melanoma
Why it's listed: “Patients with unresectable or metastatic melanoma with an NF1 mutation; Variance of NF1 of unknown/ uncertain significance will not be eligible; The genetic ana…”
RecruitingNCT02544022
Development and Validation of Patient Reported Outcome (PRO) Measures for Individuals With Neurofibromatosis 1 (NF1) and Plexiform Neurofibromas (pNFs)
Neurofibromatosis 1 · Plexiform Neurofibromas
Why it's listed: “NF1 gene, PER the Neurofibromatosis Diagnostic Criteria AND \>=1 plexiform neurofibroma in any loc…”
RecruitingPhase 1, Phase 2NCT06666348
Phase 1/2 Study of Mirdametinib + Vinblastine for Newly Diagnosed/Previously Untreated PLGG + Activation of MAPK
Pediatric Low-grade Glioma
Why it's listed: “Participants must have PLGG with NF1 gene mutation (based on clinical NIH criteria, germline NF1 mutation or molecular analysis of…”
RecruitingPhase 1NCT06961565
PAS-004 in Adults Who Have Neurofibromatosis Type 1 With Plexiform Neurofibromas
NF1 Mutation · Neurofibroma Plexiform · Neurofibroma, Plexiform
Why it's listed: “…c parent with confirmed diagnosis of NF1 viii. Genetic testing demonstrating a pathogenic NF1 germline mutation per CLIA-certified laboratory (or equivalent) testing.”
RecruitingNCT07221331
Prevalence, Clinical Characteristics, Progression, and Management of Neurofibromatosis Type 1 in Egypt (NF1-Egy)
Neurofibromatosis Type 1
Why it's listed: “Neurofibromatosis type 1 (NF1), a genetic disorder, results from NF1 gene mutations with nearly complete penetrance (1). NF1 is considered common as a rare disease…”
RecruitingPhase 1, Phase 2NCT05849662
A Phase I/II Study of Trametinib and Azacitidine for Patients With Newly Diagnosed Juvenile Myelomonocytic Leukemia
Leukemia, Juvenile Myelomonocytic · JMML · JCML
Why it's listed: “Clinical diagnosis of neurofibromatosis type 1 or germline NF1 mutation and loss of heterozygosity of NF1 or somatic biallelic loss of NF1”
RecruitingPhase 1NCT06299839
PAS-004 in Patients With Advanced Solid Tumors
RAS Mutation · NF1 Mutation · RAF Mutation
Why it's listed: Lists NF1 among its conditions or keywords
RecruitingPhase 1, Phase 2NCT07539441
A Study of Mirdametinib in People With Central Nervous System Tumors
Central Nervous System Tumors · Glioma
Why it's listed: “Have: somatic NF1 mutation as per next-generation sequencing (such as MSK Impact) --or- germline NF1 as per NIH clin…”
RecruitingPhase 1, Phase 2NCT06194929
Defactinib and Avutometinib, With or Without Encorafenib, for the Treatment of Patients With Brain Metastases From Cutaneous Melanoma
Cutaneous Melanoma · Brain Metastases
Why it's listed: “Must have a tumor with a known RAS, BRAF, or NF1 mutation or triple wildtype status using validated testing methods prior to enrollment. Cohorts wi…”
RecruitingPhase 1, Phase 2NCT04750928
Cyclin-Dependent Kinase (CDK)4/6 Inhibitor Abemaciclib for Neurofibromatosis Type I (NF1) Related Atypical Neurofibromas
Neurofibromatosis 1
Why it's listed: “…e., participants must have at least two of the diagnostic criteria for NF1 or a confirmed NF1 mutation from a CLIA-certified laboratory:”
RecruitingPhase 2NCT05735717
MT2021-08T Cell Receptor Alpha/Beta Depletion PBSC Transplantation for Heme Malignancies
Hematologic Malignancy · Acute Leukemia · Remission
Why it's listed: Lists NF1 among its conditions or keywords
RecruitingPhase 1NCT03454035
Ulixertinib/Palbociclib in Patients With Advanced Pancreatic and Other Solid Tumors
Tumor, Solid · Pancreatic Cancer · Melanoma
Why it's listed: “…/Q61, KRASG12/G13, HRASG12/G13, any amplifications of the NRAS, KRAS, or HRAS genes. For NF1 mutations, subjects with loss-of-function NF1mutations and without any BRAFV600 mutations will be e…”
RecruitingPhase 2NCT05331105
HL-085 in Adults With Neurofibromatosis Type 1 (NF1) and Inoperable Plexiform Neurofibromas
Neurofibromatosis 1 · Plexiform Neurofibromas
Why it's listed: “…must have inoperable and symptomatic plexiform neurofibromas(PN), and patients must have NF1 mutation or meet at least 1 of the following NF1 diagnostic criteria:”
Opening soonPhase 2NCT06620354
Clinical Study on the Treatment of Type I Neurofibromatosis With Smeitinib Hydrosulfate Capsule
Neurofibromatosis 1
Why it's listed: “…ions, such as sphenoid dysplasia, anterolateral tibial curvature; Pathogenic heterozygote NF1 variant with 50% allele variant fraction in normal tissues (such as white blood cells); NF1 is di…”
Opening soonPhase 2NCT06621082
The Clinical Study of the Treatment of Patients With Type I Neurofibromatosis With Smetinib Hydrosulfate Capsule
Neurofibromatosis 1
Why it's listed: “…ions, such as sphenoid dysplasia, anterolateral tibial curvature; Pathogenic heterozygote NF1 variant with 50% allele variant fraction in normal tissues (such as white blood cells); NF1 is di…”
Opening soonPhase 2NCT07521657
Efficacy of Mirdametinib Alone or Combination With Radiotherapy for Germline and Sporadic NF1-Altered High-Grade Glioma
Neurofibromatosis 1 (NF1)
Why it's listed: “…e. Tumor Next Generation Sequencing (NGS) must demonstrate at least one pathogenic/likely pathogenic NF1 alteration (known or suspected to confer loss of function) at time of first or recurrent…”

All conditions linked to NF1 gene mutations

Orphanet records how each gene relates to each condition. Orphanet links NF1 to 11 rare conditions and lists variants in the gene as a cause of 8 of them.

  • Causes it. Disease-causing variants in this gene are a direct cause of the condition.
  • Causes it, acquired. Variants that arise during life in the tumor or affected cells cause the condition. They are not inherited.
  • Plays a part. Orphanet lists the gene as shaping the condition, often as one of several genes in a missing or extra piece of a chromosome.
  • Tested as a marker. The gene is tested to help diagnose or classify the condition rather than as its cause.
Hereditary pheochromocytoma-paragangliomaCauses itTrial Friend pageOrphanet
Mosaic neurofibromatosis type 1Causes itTrial Friend pageOrphanet
Neurofibromatosis type 1 due to NF1 mutation or intragenic deletionCauses itTrial Friend pageOrphanet
Neurofibromatosis-Noonan syndromeCauses itTrial Friend pageOrphanet
Alveolar rhabdomyosarcomaCauses it, acquiredOrphanet
Embryonal rhabdomyosarcomaCauses it, acquiredOrphanet
Juvenile myelomonocytic leukemiaCauses it, acquiredOrphanet
Pleomorphic rhabdomyosarcomaCauses it, acquiredOrphanet
17q11 microdeletion syndromePlays a partOrphanet
17q11.2 microduplication syndromePlays a partOrphanet
High-grade astrocytoma with piloid featuresTested as a markerOrphanet

NF1 genetic test results and what a variant can mean

Labs sort each variant they find into 5 groups, from pathogenic and likely pathogenic through uncertain significance to likely benign and benign. Only the first 2 are usually treated as the cause of a condition. A variant of uncertain significance, or VUS, is one without enough evidence either way yet, and labs can reclassify it as research builds.

A genetic counselor or your doctor can explain what a specific result means for you and your family. Our genetic testing guide covers the terms, and MedlinePlus Genetics from the National Library of Medicine has a plain-language page on NF1.

NF1 gene questions

What does the NF1 gene do?

NF1 makes neurofibromin, a tumor suppressor protein. It helps keep cells from growing and dividing too fast by turning off a growth-signaling protein called Ras. This summary follows MedlinePlus Genetics from the U.S. National Library of Medicine.

Are there clinical trials for people with NF1 gene variants?

As of September 29, 2026, 16 recruiting or soon-opening trials on ClinicalTrials.gov name NF1 as a gene. Each one is listed on this page with the words from the trial that mention the gene. ClinicalTrials.gov also lists 55 open trials for Neurofibromatosis Type 1 and 44 for Pheochromocytoma, and Match Me on Trial Friend can check those against age, sex, location and treatment history.

What conditions are linked to the NF1 gene?

Orphanet links NF1 to 11 rare conditions and lists variants in the gene as a cause of 8 of them. They include Hereditary pheochromocytoma-paraganglioma, Mosaic neurofibromatosis type 1, Neurofibromatosis type 1 due to NF1 mutation or intragenic deletion, Neurofibromatosis-Noonan syndrome, Alveolar rhabdomyosarcoma, Embryonal rhabdomyosarcoma and 5 more. Orphanet is the European rare disease database run by INSERM in Paris.

How is Neurofibromatosis Type 1 inherited?

The inheritance pattern is autosomal dominant. One disease-causing variant can be enough to cause the condition. About half of cases are de novo NF1 variants; the diagnosis can be made clinically, with NF1 testing used to confirm.

How is Pheochromocytoma inherited?

The inheritance pattern is autosomal dominant. One disease-causing variant can be enough to cause the condition. About 35% of cases are hereditary, so germline panel testing is recommended for essentially all patients.

What does an NF1 variant of uncertain significance mean?

A variant of uncertain significance, or VUS, is a change in the gene that labs don't yet have enough evidence to call disease-causing or harmless. It is not used on its own to diagnose a condition, and labs can reclassify it as research builds. A genetic counselor can explain what a specific result means for you and your family.

Sources

  • Gene and condition links from Orphadata (Orphanet, INSERM US14), used under CC BY 4.0, read September 29, 2026.
  • Trials from ClinicalTrials.gov, read September 29, 2026.
  • NF1 gene, MedlinePlus Genetics, U.S. National Library of Medicine.
  • Inheritance and gene notes from the Trial Friend condition pages above, each checked against genetics references.

Other gene pages

The gene search covers every gene Orphanet links to a rare disease.