Otsuka Pharmaceutical

Otsuka Pharmaceutical works on 9 rare diseases tracked on Trial Friend, including Focal Segmental Glomerulosclerosis, Geographic Atrophy, IgA Nephropathy and 6 more, with 15 recruiting clinical trials and 4 FDA-approved rare disease drugs.

Otsuka Pharmaceutical develops treatments for rare genetic and renal diseases. Key products include JYNARQUE (tolvaptan), the first treatment to slow kidney function decline in autosomal dominant polycystic kidney disease (approved 2018), and Voyxact (sibeprenlimab), approved in November 2025 for IgA nephropathy. The company also has repinatrabit in Phase 3 for phenylketonuria (initiated December 2025).

Type
Diversified Pharma
Ticker
4578
Headquarters
Tokyo, Japan
Founded
1964
15
Active Rare Disease Trials
4
Approved Rare Disease Drugs
9
Rare Diseases in Portfolio
62
Years Active

Focus areas at Otsuka Pharmaceutical

Within its broader pharmaceutical portfolio, Otsuka Pharmaceutical has active clinical trial programs and drug development efforts across 9 rare diseases, including Focal Segmental Glomerulosclerosis, Geographic Atrophy, IgA Nephropathy, IgA Vasculitis with Nephritis, Myelodysplastic Syndromes, and 4 additional rare conditions. These programs may span orphan drug designation, novel therapeutic mechanisms, and precision medicine approaches targeting the underlying causes of each disease.

The clinical trials section below shows all active and recruiting studies sponsored by Otsuka Pharmaceutical, sourced live from ClinicalTrials.gov. Each trial includes its current recruitment status, study phase (Phase 1 through Phase 4), conditions under investigation, and the number of active trial sites. The FDA-approved drugs section lists treatments that have received U.S. Food and Drug Administration approval, with brand names, generic names, approval dates, and matched rare disease indications from the openFDA database.

Otsuka Pharmaceutical is headquartered in Tokyo, Japan, founded in 1964, publicly traded under the ticker symbol 4578. The company maintains a dedicated rare disease division alongside its broader therapeutic portfolio, working to bring innovative treatments to patients with conditions that have historically had limited or no treatment options.

Otsuka Pharmaceutical Drug Pipeline

Otsuka Pharmaceutical has 15 active clinical trials across 3 development stages, with 15 currently recruiting participants. Clinical trials advance through phases: Phase 1 tests safety in a small group, Phase 2 evaluates effectiveness and side effects, Phase 3 confirms benefit in a larger population, and Phase 4 monitors long-term safety after FDA approval.

Note: This pipeline includes all of Otsuka Pharmaceutical's active interventional trials, not only those targeting rare diseases. We show the full pipeline because a company's broader research activity, therapeutic expertise, and development infrastructure directly shape its ability to advance rare disease programs. A strong overall pipeline often signals deeper clinical operations, faster enrollment capabilities, and greater commitment to bringing new treatments to patients.

Understand Otsuka Pharmaceutical's pipeline
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3
Early Phase / Phase 13 trials
Recruiting
Systemic Lupus Erythematosus (SLE)+2 more
Recruiting
Lower-risk Myelodysplastic
Recruiting
2
Phase 22 trials
Recruiting
T-cell Non-Hodgkin Lymphoma+1 more
Recruiting
10
Phase 310 trials
Autosomal Recessive Polycystic Kidney (ARPKD)
Recruiting
Recruiting
Attention-Deficit Hyperactivity Disorder(ADHD)
Recruiting

Otsuka Pharmaceutical Clinical Trials (15)

Active and recruiting clinical trials sponsored by Otsuka Pharmaceutical, sourced live from ClinicalTrials.gov. Each trial card shows the study phase, current recruitment status, conditions under investigation, study locations, eligibility criteria, and a direct link to the full ClinicalTrials.gov record. You can also download a one-page PDF summary to share with your doctor.

Note: Recruitment statuses on ClinicalTrials.gov may not immediately reflect recent FDA decisions, sponsor announcements, or enrollment changes. Always confirm a trial's current status directly with the study coordinator.

Ask about Otsuka Pharmaceutical's trials
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RECRUITINGPHASE1Recently updatedNCT07713758

A Trial to Examine if Repinatrabit is Processed Differently in Adults With Reduced Liver or Kidney Function Compared to Adults With Normal Liver and Kidney Function

Intervention: Repinatrabit

This trial is intended to understand how the body processes repinatrabit in people with moderate liver impairment and severe kidney impairment and also to compare these results with people of similar age, weight, and sex who have normal liver function.

Ages 18 Years - 65 Years1 location
View full study
RECRUITINGPHASE3Recently updatedNCT04782258

A Study to See if Tolvaptan is Safe in Infants and Children Who at Enrollment Are 28 Days to Less Than 18 Years Old With Autosomal Recessive Polycystic Kidney Disease (ARPKD)

Intervention: Tolvaptan Suspension, Tolvaptan Tablets

Autosomal Recessive Polycystic Kidney (ARPKD)

To evaluate the pharmacodynamics and safety of tolvaptan in pediatric subjects with ARPKD

Ages 28 Days - 18 Years23 locations
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ACTIVE NOT RECRUITINGPHASE1Recently updatedNCT06799520

A Phase 1 Trial to Evaluate the Safety, Tolerability, Pharmacodynamics, Pharmacokinetics, and Immunogenicity of VIS171 in Participants With Autoimmune Disease(s)

Intervention: VIS171

Systemic Lupus Erythematosus (SLE)Alopecia Areata (AA)Immune-mediated Focal Segmental Glomerulosclerosis (FSGS)

The purpose of this trial is to measure safety and tolerability of subcutaneous (SC) VIS171 in combination with standard of care in participants with autoimmune disease(s). The total duration of the clinical trial for each participant will be up to approximately 9 to 12 months.

Ages 18 Years - 75 Years6 locations
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ACTIVE NOT RECRUITINGPHASE3Recently updatedNCT05248646

Trial of Sibeprenlimab in the Treatment of A Nephropathy (IgAN)

Intervention: Sibeprenlimab 400 mg, Placebo

To Evaluate the Efficacy and Safety of Sibeprenlimab Administered Subcutaneously in Subjects with Primary Immunoglobulin A Nephropathy

Ages 18 Years+308 locations
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RECRUITINGPHASE3Recently updatedNCT06971731

A Study of JNT-517 in Participants With Phenylketonuria (PKU)

Intervention: JNT-517 Tablet, JNT-517 Tablet, Placebo Tablet: BID

The goal of this Phase 3, randomized study is to assess the safety, efficacy, tolerability, and pharmacokinetics (PK) of oral JNT-517 in adults (18 years of age or older) with PKU. Participants will receive either JNT-517 or placebo and will be blinded to their treatment assignment. Participants will have a 2 in 3 (or approximately 67%) chance of receiving JNT-517 during the first part of the study which will last approximately six weeks. During the second part of the study every participant who continues in the study will receive one of two doses of JNT-517 for an additional 46 weeks. The study requires a screening period of up to 35 days to ensure dietary stabilization and amino acid levels required to meet study eligibility. In total, participation in the study could last for up to 400 days. Participants will: Take 75 mg JNT-517 or 150 mg JNT-517, or a placebo BID (2x per day) for approximately 365 days; Visit the clinic or have a mobile health nurse visit your home for checkups and tests; Collect urine sample at home and bring to clinic on specified days; Keep a food diary 3 days before each study visit

Ages 18 Years+26 locations
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RECRUITINGPHASE3Updated a few months agoNCT06628128

A Long-Term Study of JNT-517 in Participants With Phenylketonuria

Intervention: JNT-517

The goal of this Phase 3, open-label study is to evaluate the long-term safety of JNT-517 in pediatric and adult participants with Phenylketonuria (PKU) after completion of either Study JNT517-101 (NCT05781399) or JNT517-201 (NCT06637514) as well as participants who have not participated in a prior JNT-517 study. In this trial, all participants will receive JNT-517 using age- and weight-banded dosing as outlined in the protocol, regardless of any dose received in a previous study.

Ages 4 Years+12 locations
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RECRUITINGPHASE3No updates in a whileNCT07087327

A Long-term Trial of EB-1020 in Pediatric Patients With ADHD

Intervention: EB-1020 (Centanafadine) low dose, EB-1020 (Centanafadine) high dose

Attention-Deficit Hyperactivity Disorder(ADHD)

The purpose of this study is to evaluate the safety of long-term administration of mainly high doses of EB-1020 over 52 weeks in pediatric ADHD patients.

Ages 6 Years - 17 Years1 location
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Otsuka Pharmaceutical FDA-Approved Drugs (4)

Medications developed or marketed by Otsuka Pharmaceutical that have received U.S. Food and Drug Administration approval. Drug data is sourced from the openFDA database and includes brand names, generic names, approval dates, and matched rare disease indications. Where a drug treats a condition covered by Trial Friend, the disease name links directly to that disease page.

Drug NameBrand NameRare DiseasesApproval Date
ARIPIPRAZOLE
Atypical Antipsychotic [EPC]
Abilify Asimtufii
intramuscular
Apr 27, 2023
TOLVAPTAN
Vasopressin V2 Receptor Antagonist [EPC]
Jynarque
oral
Apr 23, 2018
BREXPIPRAZOLE
Atypical Antipsychotic [EPC]
Rexulti
oral
Jul 10, 2015
SIBEPRENLIMABVOYXACT
subcutaneous
Nov 25, 2025

Otsuka Pharmaceutical Trial Locations

Otsuka Pharmaceutical clinical trials are running at 434 sites in 35 countries. Click any country to drill down by state, city, and individual research facility. Proximity to a trial site is one of the most important factors in deciding whether to participate.

United States
89▼
Japan
74▼
Australia
27▼
China
25▼
Spain
22▼
South Korea
17▼
France
16▼
India
15▼
Italy
14▼
Brazil
11▼
Canada
10▼
United Kingdom
9▼

Rare Disease Focus Areas (9)

Diseases targeted by Otsuka Pharmaceutical's clinical trial and drug development programs

Focal Segmental GlomerulosclerosisKidney & Renal

Focal Segmental Glomerulosclerosis (FSGS) is a kidney disease characterized by scarring of some glomeruli, the tiny filtering units that remove waste from the blood. The disease can develop on its own...

Prevalence: Approximately 7% of all kidney biopsies in the United States show FSGS; incidence is 0.2-1.7 cases per 100,000 person-years
Geographic AtrophyEye & Vision

Geographic atrophy is the advanced form of dry age-related macular degeneration, characterized by progressive loss of retinal pigment epithelium, photoreceptors, and choriocapillaris in well-defined a...

Prevalence: Approximately 1 million people in the U.S.; affects about 20% of those with age-related macular degeneration
IgA NephropathyKidney & Renal

IgA nephropathy is the most common primary glomerulonephritis worldwide, caused by abnormal IgA1 antibodies depositing in the kidney's mesangium, activating complement pathways and triggering inflamma...

Prevalence: Incidence is about 1 in 100,000 people per year in the U.S. (IgA Nephropathy Foundation); cumulative U.S. prevalence is estimated at roughly 130,000 to 150,000 cases. Significantly more common in East Asian and Pacific Islander populations, with reported incidence up to 4 times higher.
IgA Vasculitis with NephritisKidney & Renal

IgA vasculitis is a small-vessel vasculitis characterized by IgA immune complex deposition in kidneys and other organs. The condition manifests with purpura, arthritis, and glomerulonephritis. Most pa...

Prevalence: About 3 to 27 new cases per 100,000 children each year; the most common vasculitis of childhood
Myelodysplastic SyndromesBlood & Immune

Myelodysplastic syndromes are a group of blood cancers in which the bone marrow fails to produce enough healthy blood cells. Immature blood cells do not develop properly and either die in the bone mar...

Prevalence: 10,000 to 15,000 new cases annually in the U.S.; estimated 60,000 to 170,000 Americans living with MDS
PhenylketonuriaMetabolic & Lysosomal

Phenylketonuria is an inherited metabolic disorder caused by a missing enzyme that prevents the body from properly breaking down the amino acid phenylalanine. This causes a buildup that can damage the...

Prevalence: 1 in 10,000 to 15,000 newborns in the U.S.

Patient Resources

Organizations and resources related to Otsuka Pharmaceutical's rare disease focus areas

Frequently Asked Questions About Otsuka Pharmaceutical

Common questions about Otsuka Pharmaceutical's rare disease programs, clinical trials, and treatments.